Visual Loss Post Ross Procedure in an Adolescent With Newly Diagnosed Mucopolysaccharidosis Type II.
case_report · Level V
Where this comes from
- Record sourced from PubMed, PMID 30953652.
- Also identified by DOI 10.1016/j.athoracsur.2019.03.011.
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Abstract
Perioperative visual loss is a rare but serious complication after cardiac surgery. The etiology is not fully understood, and there is no consensus on the optimal management of this condition. A 15-year-old male patient developed severe visual impairment attributed to nonarteritic anterior ischemic optic neuropathy after a Ross aortic root replacement procedure. A new diagnosis of the lysosomal storage disorder, mucopolysaccharidosis type II (Hunter syndrome), was subsequently made, raising questions about the pathogenesis of this devastating postoperative complication.
Medical subject headings
- Blindness
- Cardiac Surgical Procedures
- Mucopolysaccharidosis II
- Postoperative Complications