A Potentially Malignant Giant Esophageal Paraganglioma.

Arbel Rubinstein, Tammi; Kouniavsky, Gennady; Kanengisser Pines, Bibi; Idelevich, Efraim; Lazar, Li Or; Elami, Amir; Bar, Ilan; Pines, Guy · Ann Thorac Surg · 2019

case_report · Level V

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Abstract

Paragangliomas are rare neuroendocrine tumors derived from extraadrenal autonomic paraganglia, which may secrete catecholamines. They are potentially metastatic and require very long-term follow-up. Esophageal paragangliomas are extremely rare and present a diagnostic challenge. Lack of clinical suspicion and unrecognized catecholamine hypersecretion may lead to hemodynamic instabilities during surgery. Two patients with esophageal paragangliomas were previously reported. We report a 39-year-old man with a giant high-risk esophageal paraganglioma who underwent a hybrid minimally invasive 3-hole esophagectomy.

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