Management of Multiple Secreting Paragangliomas in a Succinate Dehydrogenase Subunit D (SDHD) Variant Carrier.

Rijken, Johannes A; de Vos, Berry; Leemans, C René; Zwezerijnen, G J C Ben; de Graaf, Pim; Hensen, Erik F; Dreijerink, Koen M A; Dickhoff, Chris et al. · Ann Thorac Surg · 2020

case_report · Level V

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Abstract

Management of functional intrathoracic sympathetic paragangliomas in succinate dehydrogenase subunit D (SDHD) mutation carriers is challenging, and there is no uniform guideline for treatment to date. The risks of potential malignant behavior and long-term cardiovascular morbidity have to be weighed against the risks of treatment complications. We report the multidisciplinary and shared decision-making approach that resulted in successful surgical removal of 3 paragangliomas in a SDHD mutation carrier.

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