Case of Hemorrhagic Moyamoya Disease Associated with Von Willebrand Disease.
case_report · Level V
Where this comes from
- Record sourced from PubMed, PMID 31326638.
- Also identified by DOI 10.1016/j.wneu.2019.07.106.
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Abstract
Association of moyamoya disease (MMD) with von Willebrand disease (vWD) is extremely rare. We first report a 27-year-old female case of MMD concurrent with vWD type 1, which presented as hemorrhagic stroke. The patient underwent a revascularization surgery with perioperative replacement therapy of von Willebrand factor and coagulation factor VIII. No hemorrhagic complications occurred. The patient overcame postoperative transient neurological events and fully recovered. We discuss appropriate perioperative supplementation of coagulation factors for a revascularization surgery for MMD with vWD.
Medical subject headings
- Hemorrhage
- Moyamoya Disease
- von Willebrand Disease, Type 1