A rarer association of eosinophilic fasciitis.
case_report · Level V
Where this comes from
- Record sourced from PubMed, PMID 31334201.
- Also identified by DOI 10.4103/jfmpc.jfmpc_281_19 and PMC identifier 6618199.
- Licence recorded as CC BY-NC-SA.
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Abstract
Eosinophilic fasciitis (EF, also called Shulman syndrome) is a rare connective tissue disorder with poorly understood pathogenesis and unknown etiology. EF is characterized initially by limb or trunk erythema and edema and later by collagenous thickening of the subcutaneous fascia. Here, we present the case of a 16-year-old boy who presented with typical clinical features of EF with a history of typical trigger factor - preceding strenuous physical activity and had a rarer atypical association of hypercalcemia and raised angiotensin converting enzyme (ACE) levels.