Sporadic Meningioangiomatosis Presenting as a Middle Cranial Fossa Arachnoid Cyst.

Abstract

Meningioangiomatosis is an extremely rare meningovascular disease of the central nervous system that is characterized by the proliferation of leptomeninges, cortical vessels, and perivascular spindled cells. Although it is a benign, neoplastic disorder that carries a good prognosis after surgical excision, initial diagnosis may be challenging as radiologic findings are often variable and nonspecific. In this report, we describe an unusual presentation of meningioangiomatosis presenting as a symptomatic middle cranial fossa arachnoid cyst. In view of the unexpected diagnosis and infrequency of this condition, the case is discussed in collaboration with current literature and management strategies.