Hand Deformities in Hajdu-Cheney Syndrome: A Case Series of 3 Patients Across 3 Consecutive Generations.

Jiménez, Isidro; Medina-Gontier, Julie; Caballero, Jonathan; Medina, José · J Hand Surg Am · 2021

case_series · Level IV

Where this comes from

Abstract

Hajdu-Cheney syndrome is a rare condition characterized by acro-osteolysis, osteoporosis, and multiple craniofacial anomalies. The goal of treatment is to reduce the associated symptoms and to prevent osteoporotic fractures. This is a report of 3 patients across consecutive generations demonstrating variable phenotypic severity. The hand surgeon was the first medical care provider visited by the patients because of the shortening of the fingers.

Medical subject headings

Anatomy