Familial Os Odontoideum.

Prasad, Apurva; Shah, Abhidha; Sasane, Sumeet; Goel, Atul · World Neurosurg · 2020

case_report · Level V

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Abstract

To add to the confusion in the debate on pathogenesis of os-odontoideum, an additional report of its occurrence in two members of the same family is reported. This is a report of a rare coincidence wherein both father (51 years old) and daughter (25 years old) were diagnosed to have os odontoideum and presented with crippling neurologic deficits. Following atlantoaxial fixation, both recovered in their symptoms. Investigations revealed no genetic abnormality. Literature on the subject is briefly reviewed.

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