ITK deficiency presenting as autoimmune lymphoproliferative syndrome.

Wallace, Jacqueline G; Alosaimi, Mohammed F; Khayat, Claudia Djambas; Jaber, Faris; Almutairi, Abduarahman; Beaussant-Cohen, Sarah; Pinkus, Geraldine; Fleming, Mark et al. · J Allergy Clin Immunol · 2021

Where this comes from

Abstract

A patient with a novel homozygous mutation in <i>ITK</i> presented with autoimmune lymphoproliferative syndrome, and had impaired TCR-driven Fas ligand upregulation, providing a mechanism for the T cell lymphoproliferation.

Medical subject headings