Multifocal Calcifying Fibrous Tumor at Seven Intrathoracic Sites in One Patient.
case_report · Level V
Where this comes from
- Record sourced from PubMed, PMID 32682754.
- Also identified by DOI 10.1016/j.athoracsur.2020.05.100 and PMC identifier 9362959.
- No licence information is recorded for this record.
- Because redistribution is not established, this page shows the abstract only. Follow the links below for the full text.
Abstract
Calcifying fibrous tumors are rare lesions that occur throughout the body. A 35-year-old man presented with exertional dyspnea. Computed tomography showed a polypoid mass abutting pericardium, diaphragm, and left chest wall, and a pleural-based lesion adjacent to T12. Thoracoscopy revealed a large mass with diaphragmatic stalk, two pleural-based nodules, and four diaphragmatic nodules. Pathologic analysis of resected lesions showed calcifying fibrous tumors. Three lesions contained heterogenous mutations associated with this tumor type. The patient is disease free 1 year later. Calcifying fibrous tumors should be recognized as rare multifocal pleural and diaphragmatic-based tumors. Complete resection leads to excellent survival for patients with this uncommon disease.
Medical subject headings
- Calcinosis
- Pleura
- Pleural Neoplasms
- Thoracoscopy
- Tomography, X-Ray Computed