Glioblastoma in Beckwith-Wiedemann syndrome: first case report and review of potential pathomechanisms.

Weir, Peter; Kumaria, Ashwin; Mohmed, Alhassan; Javed, Shazia; Paine, Simon; Byrne, Paul · Acta Neurochir (Wien) · 2022

case_report · Level V

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Abstract

Beckwith-Wiedemann syndrome (BWS) is a rare congenital overgrowth syndrome associated with certain childhood tumours. We present the case of a 36-year-old lady with BWS who developed a left frontoinsular secondary glioblastoma. This is the first case report in the literature of glioblastoma associated with BWS. We explore similarities in the molecular pathomechanisms of BWS and glioblastoma.

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