Detection and characterization of low-level mosaicism among clinically unaffected parents of 'sporadic' epidermolysis bullosa simplex cases.

Chen, Fuying; Deng, Dan; Pan, Chaolan; Yao, Zhirong; Gu, Yan; Li, Ming · Br J Dermatol · 2022

case_report · Level V

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Abstract

In this study, two (18.2%) clinically unaffected parents from 11 trios were identified with mosaic KRT14 variants.To our knowledge, this is the first report to study the proportion of low-level mosaicism in the clinically unaffected parents whose children were previously regarded as sporadic EBS cases.

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