Relapsing Polychondritis With Palmoplantar Pustulosis.

Comarmond, Cloé; Chimon, Alice; Salfrant, Maxime; Sène, Damien · J Rheumatol · 2023

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Abstract

Palmoplantar pustulosis (PPP) is a very rare cutaneous manifestation observed during relapsing polychondritis (RP),<sup>1,2</sup> not found in other conditions associated with saddle nose (eg, granulomatosis with polyangiitis, sarcoidosis, VEXAS [vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic] syndrome, congenital syphilis, leprosy, septal abscess).