Aortic Dissection in a Young Patient With Unsuspected Aortopathy.

Perez, Yalile; Qureshi, M Yasir; Babovic-Vuksanovic, Dusica; Cannon, Bryan · Pediatrics · 2023

case_report · Level V

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Abstract

Aortic dissection is often a fatal condition if not recognized and treated emergently. Fortunately, it is extremely rare in children and adolescents. We report a case of an adolescent boy who survived an aortic dissection due to severe aortic root dilation. A comprehensive history and physical examination, including family history, can facilitate an early diagnosis of connective tissue diseases, such as Loeys-Dietz syndrome (LDS).

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