Extracorporeal Membrane Oxygenation-Dependent Fulminant Melioidosis From Caspase 4 Mutation Reversed by Interferon Gamma Therapy.

Amali, Aseervatham Anusha; Ravikumar, Sharada; Chew, Wei Leong; Tan, Zhaohong; Sam, Qi Hui; Chen, Kaiwen W; Boucher, Dave; MacLaren, Graeme et al. · Clin Infect Dis · 2024

case_report · Level V

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Abstract

We describe bedside-to-bench immunological and genetic elucidation of defective pyroptosis attributable to novel caspase 4 defect mediating pathogen-triggered inflammatory programmed cell death, in the setting of severe pneumonia and abscess-forming melioidosis in an overtly healthy host failing to clear Burkholderia pseudomallei infection, and how targeted adjunctive biological therapy led to a successful outcome.

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