Recurrent benign fibrous histiocytoma of the bone benefits from denosumab followed by malignant transformation: a case report.

Laureline, Wetterwald; Patrick, Omoumi; Tu, Nguyen; Stephane, Cherix; Ana, Dolcan; Daniela, Ferraro; Chiara, Saglietti; Igor, Letovanec et al. · Skeletal Radiol · 2024

case_report · Level V

Where this comes from

Abstract

Benign fibrous histiocytoma of the bone (BFHB) is a rare mesenchymal tumor, representing less than 1% of all benign bone tumors. This controversial entity is characterized by a mixture of fibroblasts arranged in a storiform pattern, varying amounts of osteoclast-type giant cells and foamy macrophages. Curettage or simple resection is usually curative. However, it was reported that up to 11% of the patients suffer from relapse. Here, we report a case of malignant transformation of BFHB after long-lasting disease stabilization under denosumab therapy.

Medical subject headings