Bilateral Sudden on Chronic Hearing Loss as an Auditory Manifestation of Mitochondrial DNA Mutations.

Liu, Chin-Nung; Yan, Hong-Yu; Liao, Steven Chun-Kang; Tsai, Cheng-Yu; Tseng, Li-Huei; Lin, Pei-Hsuan; Lee, Ni-Chung; Wu, Chen-Chi · Laryngoscope · 2026

case_series · Level IV

Where this comes from

Abstract

We presented a series of patients with a mitochondrial DNA mutation who presented to our clinic with sudden bilateral sudden on chronic sensorineural hearing loss; these patients responded well to cochlear implantation. In cases of sudden sensorineural hearing loss-particularly when clinical features raise suspicion for an underlying mitochondrial disorder-genetic testing may offer valuable diagnostic insight and assist in guiding appropriate management strategies.

Medical subject headings