Congenitally corrected transposition of the great arteries: outcomes after single ventricle palliation.

Abstract

Congenitally corrected transposition of the great arteries (ccTGA) is a rare congenital cardiac anomaly. As a viable alternative for complex anatomical variants, the outcomes of single-ventricle palliation (SVP) in ccTGA patients remain poorly defined. We conducted a single-center retrospective analysis of ccTGA patients who underwent SVP between January 2004 and December 2020. A total of 73 patients were included. Patients with ccTGA undergoing SVP demonstrated excellent early and mid-term outcomes, with no observed mortality and freedom from MAEs of 96.0%, 93.6%, and 78.0% at 5, 10, and 15 years postoperatively, respectively. SVP can achieve excellent early and mid-term outcomes in carefully selected ccTGA patients. When complex biventricular repair is not feasible, SVP represents a safe and effective alternative. Single-ventricle palliation can achieve excellent outcomes in selected congenitally corrected transposition of the great arteries. When complex biventricular repair is not feasible, SVP represents a safe and effective alternative.