New pathogenic PTPN2 variant leading to childhood interstitial lung disease.

Rowbotham, Nicola Jane; Jeanpierre, Marie; Bush, Andrew; Jagani, Sumit; Jones, Gabriela; Warrier, Kishore; Parlato, Marianna; Rieux-Laucat, Frederic et al. · Thorax · 2026

case_report · Level V

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Abstract

Protein tyrosine phosphatase non-receptor type 2 (<i>PTPN2</i>) is a tyrosine phosphatase involved in T cell receptor signal transduction and cytokine response. Loss of function variants have previously been linked with immune mediated diseases such as inflammatory bowel disorders, rheumatoid arthritis and type 1 diabetes. We present a case of childhood interstitial lung disease with a newly identified pathogenic <i>(PTPN2</i>) gene variant in a boy aged 4 years.