Primary Pseudomyogenic Hemangioendothelioma of the Cranium: Findings on FDG-PET/CT.

Abstract

Pseudomyogenic hemangioendothelioma (PMH) is an extremely rare intermediate-grade vascular neoplasm. It often arises in the distal extremities and characteristically involves multiple tissue planes. It has a male predominance, and usually affects individuals in the second to fourth decades of life. Here we report a 54-year-old man who presented with an occipital mass lasting for three months. On imaging studies, the occipital bone tumors were expansile, well circumscribed and lytic, accompanied by adjacent scalp and subcutaneous nodules, with marked enhancement of the lesion upon contrast administration. FDG PET/CT demonstrated high FDG affinity in the lesion. Surgical pathology diagnosed as PMH.