Sudden Acute Liver Failure in Citrullinemia Type 1: An Argument for Earlier Liver Transplantation?

Eldredge, Jessica A; Dhawan, Anil; Deheragoda, Maesha; Heaton, Nigel D; Cortes-Cerisuelo, Miriam; Grünewald, Stephanie; Hadžić, Nedim; Vara, Roshni · J Pediatr · 2026

case_series · Level IV

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Abstract

Acute liver failure has been described at initial presentation of citrullinemia type 1, but recurrent hepatic decompensations during medical treatment have not been reported. We describe 5 children developing episodes of acute liver failure, including one who required emergency liver transplantation. Our findings expand the citrullinemia type 1 phenotype and support early liver transplant referral in selected cases.