De novo VPS16 missense variant causes infantile-onset dystonia with defective autophagic flux.

Gonzalez Saez-Diez, Enrique; Xue, Xutong; Tam, Amy; Kim, Hyo-Min; Carty, Siofra; Rong, Joshua; Ferrer-Socorro, Monica; Yang, Kathryn et al. · JCI Insight · 2026

case_report · Level V

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Abstract

A VPS16 gene variant causes movement disorder in an infant by blocking cellular waste clearance - confirmed in patient cells and potentially treatable with deep brain stimulation.

Medical subject headings