A patient with CHILD syndrome mimicking Hailey-Hailey disease: A diagnostic challenge.

Zhang, Xuewan; Zhong, Zemin; Wang, Huijun; Xue, Ruzeng; Lin, Zhimiao · J Am Acad Dermatol · 2026

case_report · Level V

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Abstract

Congenital hemidysplasia with ichthyosiform erythroderma and limb defects syndrome is a rare disorder in which atypical presentations may delay diagnosis. We report a molecularly confirmed case mimicking Hailey-Hailey disease without classical unilateral involvement or skeletal abnormalities. This case highlights an important diagnostic pitfall, emphasizes the value of NSDHL genetic testing, and demonstrates the clinical benefit of pathogenesis-directed topical simvastatin/cholesterol therapy.