Leukocyte adhesion deficiency mimicking Hirschsprung disease.

Rivera-Matos, I R; Rakita, R M; Mariscalco, M M; Elder, F F; Dreyer, S A; Cleary, T G · J Pediatr · 1995

case_report · Level V

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Abstract

An infant had clinical signs suggestive of Hirschsprung disease as the initial manifestation of leukocyte adhesion deficiency. Chromosome studies showed a deletion of the distal third of the long arm of one chromosome 21, and flow cytometric studies confirmed the defective expression of CD18.

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