Transmission of dystrophinopathy by X-chromosome inversion.

Konagaya, M; Honda, H; Sakai, M; Iida, M · Neurology · 1995

case_report · Level V

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Abstract

A woman had a karyotype of 46Xinv(X)(p21.2;q26.1) and mosaicism of dystrophin-negative muscle fibers. The X-chromosome inversion was transmitted to her daughter, who had an elevated serum CK. The genetic transmission as well as the probable random inactivation of the abnormal X chromosome in this mildly affected patient distinguish this case from those of dystrophinopathy with X;autosome translocations.

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