Orbital involvement in multifocal fibrosclerosis.

Aylward, G W; Sullivan, T J; Garner, A; Moseley, I; Wright, J E · Br J Ophthalmol · 1995

case_report · Level V

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Abstract

Multifocal fibrosclerosis is a condition of unknown aetiology, characterised by fibrous lesions occurring at a variety of sites. Clinical variants include retroperitoneal fibrosis, Riedel's thyroiditis, sclerosing cholangitis, and mediastinal fibrosis. Orbital pseudotumour has been reported as a manifestation of this condition. Three patients with multifocal fibrosclerosis in whom orbital involvement was the dominant feature are described.

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