Systemic vasculitis complicating infantile autoimmune enteropathy.

Jenkins, H R; Jewkes, F; Vujanic, G M · Arch Dis Child · 1994

case_report · Level V

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Abstract

An infant with unexplained sideroblastic anaemia and severe protracted diarrhoea due to autoimmune gut disease is reported. Despite treatment with an exclusion diet and immunosuppressive agents she developed a severe systemic vasculitic illness. Intensive treatment with plasmapheresis resulted in resolution of the vasculitic process but the child subsequently died after overwhelming septicaemia.

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