Amyloid polyneuropathy in two German-American families: a new transthyretin variant (Val 107).

Uemichi, T; Gertz, M A; Benson, M D · J Med Genet · 1994

case_report · Level V

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Abstract

We report studies on two German-American persons with systemic amyloidosis. Affected subjects presented with carpal tunnel syndrome in the sixth decade of life followed by peripheral neuropathy. DNA analysis of the transthyretin gene showed a new point mutation which is responsible for substitution of valine for isoleucine at position 107 of the transthyretin molecule.

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