Normal CAG repeat length in the Huntington's disease gene in senile chorea.

Shinotoh, H; Calne, D B; Snow, B; Hayward, M; Kremer, B; Theilmann, J; Hayden, M R · Neurology · 1994

case_series · Level IV

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Abstract

There is a widely held belief that most patients presenting with senile chorea have late-onset Huntington's disease (HD) with an unknown family history. We measured CAG trinucleotide repeat expansion in the HD gene in four patients with a clinical presentation of senile chorea and found that CAG repetition lengths were normal. These findings support senile chorea as being a distinct clinical entity that is nosologically separate from late-onset HD.

Medical subject headings