A cystic fibrosis patient homozygous for the new frameshift mutation 936delTA: description and clinical data.

Chillón, M; Casals, T; Giménez, J; Nunes, V; Estivill, X · J Med Genet · 1994

case_report · Level V

Where this comes from

Abstract

We report the identification of a new frameshift mutation (936delTA) in exon 6b of the CFTR gene. In the screening of 486 unrelated Spanish CF patients we found a patient homozygous for 936delTA (with consanguineous parents) and a patient heterozygous for delta F508 and 936delTA. Genotype-phenotype correlation studies showed that 936delTA is associated with pancreatic insufficiency and chronic pulmonary colonisation.

Medical subject headings