Orthopaedic manifestations in de Barsy syndrome.

Stanton, R P; Rao, N; Scott, C I · J Pediatr Orthop · 1994

case_report · Level V

Where this comes from

Abstract

de Barsy syndrome is a rare, genetically transmitted condition characterized by severe cutis laxa, joint hypermobility, growth retardation, mental retardation, and characteristic facies. Affected individuals have many orthopaedic manifestations, including developmental dysplasia of the hip, scoliosis, multiple joint dislocations and subluxations, and congenital vertical talus. The management of the orthopaedic manifestations of this syndrome is presented in two typical cases.

Medical subject headings

Anatomy