Pulmonary hypertension associated with non-cirrhotic portal hypertension in systemic lupus erythematosus.

Woolf, D; Voigt, M D; Jaskiewicz, K; Kalla, A A · Postgrad Med J · 1994

case_report · Level V

Where this comes from

Abstract

A case of non-cirrhotic portal hypertension in a patient with systemic lupus erythematosus, the first of our knowledge, is described. Severe pulmonary hypertension was associated with the portal hypertension and with markers of active auto-immunity. Pulmonary hypertension has not previously been associated with non-cirrhotic portal hypertension. The coexistence of vasculopathy of the portal and pulmonary vascular beds in this patient with active autoimmunity supports the postulate that portal-pulmonary hypertension may be immunologically mediated.

Medical subject headings