Presenile-onset cerebral adrenoleukodystrophy presenting as Balint's syndrome and dementia.
case_report · Level V
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Abstract
We describe a patient with presenile-onset cerebral adrenoleukodystrophy presenting as Balint's syndrome and dementia. There were demyelinating MRI changes in the parieto-occipital white matter bilaterally, including the splenium of the corpus callosum. Therapeutic trials using 1-deamino-(8-D-arginine)-vasopressin, very long-chain fatty acid-free diet, and gamma-globulin were of no benefit.
Medical subject headings
- Adrenoleukodystrophy
- Dementia