Autosomal dominant transmission of the Pallister-Hall syndrome.

Topf, K F; Kletter, G B; Kelch, R P; Brunberg, J A; Biesecker, L G · J Pediatr · 1993

case_report · Level V

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Abstract

We describe a 9-year-old boy and his 34-year-old father with the Pallister-Hall syndrome. The proband had precocious puberty, imperforate anus, postaxial polydactyly, hypospadias, a hypothalamic mass, and a displaced pituitary gland. The father had polydactyly, a hypothalamic mass, and a flattened pituitary gland. We conclude that the most likely cause of the Pallister-Hall syndrome is a mutation in a gene inherited in an autosomal dominant manner.

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