Multiple hamartoma syndrome with osteosarcoma.

Yen, B C; Kahn, H; Schiller, A L; Klein, M J; Phelps, R G; Lebwohl, M G · Arch Pathol Lab Med · 1993

case_report · Level V

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Abstract

Multiple hamartoma syndrome, also known as Cowden's disease, is a rare genodermatosis with characteristic mucocutaneous lesions associated with multiple internal abnormalities. We describe a patient having classic dermatologic manifestations of Cowden's disease and multiple neoplasia including follicular adenocarcinoma of the thyroid gland with lung metastasis, intraductal breast carcinoma within a fibroadenoma, and an osteosarcoma. To our knowledge, this is the first reported case of an osteosarcoma in Cowden's disease.

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