Idiopathic pulmonary hilar fibrosis: an unusual cause of pulmonary hypertension.

Espinosa, R E; Edwards, W D; Rosenow, E C; Schaff, H V · Mayo Clin Proc · 1993

case_report · Level V

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Abstract

A 37-year-old man with progressive exertional dyspnea had pulmonary hypertension associated with pulmonary arterial and venous obstruction. An autopsy revealed that the cause of death was idiopathic pulmonary hilar fibrosis, a variant of mediastinal fibrosis. Pulmonary hilar fibrosis can mimic thromboembolic pulmonary hypertension, pulmonary veno-occlusive disease, and pulmonary venous hypertension.

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