Successful medical treatment of severely decompensated Wilson disease.
case_series · Level IV
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- Record sourced from PubMed, PMID 8636833.
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Abstract
Delayed response to medical treatment sometimes leads to unnecessary liver transplantation in patients with severely decompensated Wilson disease. We report the course of five patients (mean age 13.4 years, range 11 to 15 years) with severely decompensated Wilson disease who were successfully treated medically. Prothrombin time improved after a minimum of 1 month and returned to normal within 3 months to 1 year or more.
Medical subject headings
- Anti-Bacterial Agents
- Hepatolenticular Degeneration
- Penicillamine
- Sulfates
- Zinc Compounds