Steroid-responsive pulmonary hypertension in a patient with Langerhans' cell granulomatosis (histiocytosis X).

Benyounes, B; Crestani, B; Couvelard, A; Vissuzaine, C; Aubier, M · Chest · 1996

case_report · Level V

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Abstract

We report the case of a man with biopsy-proved pulmonary Langerhans' cell granulomatosis (histiocytosis X) and pulmonary precapillary hypertension. Pulmonary vascular resistances and mean pulmonary artery pressure decreased with corticosteroid therapy and dyspnea improved.

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