Defective growth hormone secretion in children with pycnodysostosis and improved linear growth after growth hormone treatment.

Soliman, A T; Rajab, A; AlSalmi, I; Darwish, A; Asfour, M · Arch Dis Child · 1996

case_series · Level IV

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Abstract

Short stature is a characteristic feature of pycnodysostosis. We report defective growth hormone secretion in response to provocation and low insulin-like growth factor-I (IGF-I) concentration in five out of six patients with pycnodysostosis. Physiological replacement with growth hormone increased IGF-I concentration and improved linear growth in these children.

Medical subject headings