Corneal abnormalities associated with incontinentia pigmenti.

Ferreira, R C; Ferreira, L C; Forstot, L; King, R · Am J Ophthalmol · 1997

case_report · Level V

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Abstract

To report corneal abnormalities associated with incontinentia pigmenti. Two girls, aged 2 1/2 and 5 years, with incontinentia pigmenti from one family underwent a complete ophthalmic examination. We found vortex (whorl-like) epithelial keratitis characterized by epithelial microcysts that stained with fluorescein and midstromal radial mild haziness in daughters of a family with incontinentia pigmenti. Incontinentia pigmenti should be included in the differential diagnosis of children with keratitis, particularly if there is evidence of characteristic dermatologic or other systemic manifestations.

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