Congenital total lipodystrophy and peripheral pulmonary artery stenosis.

Uzun, O; Blackburn, M E; Gibbs, J L · Arch Dis Child · 1997

case_report · Level V

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Abstract

Multiple peripheral pulmonary artery stenoses were detected in three patients with congenital generalised lipodystrophy. This association, which has not been described before, may be clinically important in patients with lipodystrophy who present with impaired exercise tolerance or heart murmurs.

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