Pulmonary lymphangioleiomyomatosis and cerebrotendinous xanthomatosis: is there a link?

Dormans, T P; Verrips, A; Bulten, J; Cox, N · Chest · 1997

case_report · Level V

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Abstract

A 41-year-old woman had progressive shortness of breath. Cerebrotendinous xanthomatosis was diagnosed 4 years before. An open-lung biopsy showed the simultaneous presence of cerebrotendinous xanthomatosis and pulmonary lymphangioleiomyomatosis. This is perhaps the first time the coincidental occurrence of these two diseases is described.

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