A new mitochondrial DNA mutation associated with mitochondrial myopathy: tRNA(Leu)(UUR) 3254C-to-G.

Kawarai, T; Kawakami, H; Kozuka, K; Izumi, Y; Matsuyama, Z; Watanabe, C; Kohriyama, T; Nakamura, S · Neurology · 1997

case_report · Level V

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Abstract

We investigated a patient with mitochondrial myopathy accompanied by cardiomyopathy. Molecular analysis disclosed a C-to-G substitution at nucleotide position 3254 of the mitochondrial tRNA(Leu)(UUR). Pedigree analysis revealed that this mutation was inherited maternally. Mutation C3254G may also be a candidate for genetic defects in mitochondrial myopathy.

Medical subject headings