Chronic bullous disease of childhood and a paecilomyces lung infection in chronic granulomatous disease.
case_report · Level V
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- Record sourced from PubMed, PMID 9301356.
- Also identified by PMC identifier 1717284.
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Abstract
A 12 year old boy suffering from p67-phox deficient chronic granulomatous disease presented with a bullous skin disease and a lung infection with paecilomyces species. The histopathology of a bullous lesion showed subepidermal blister formation and microabcesses containing eosinophils in the dermal papillae. By direct immunofluorescence, linear staining of IgA at the dermal-epidermal junction was detected which confirmed the clinical diagnosis of chronic bullous disease of childhood (linear IgA dermatosis).
Medical subject headings
- Autoimmune Diseases
- Granulomatous Disease, Chronic
- Lung Diseases, Fungal
- Paecilomyces
- Skin Diseases, Vesiculobullous