Cerebral primitive neuro-ectodermal tumour following treatment of a unilateral retinoblastoma.

Dorfmüller, G; Würtz, F G; Kleinert, R; Lanner, G · Acta Neurochir (Wien) · 1997

case_report · Level V

Where this comes from

Abstract

Cerebral primitive neuro-ectodermal tumour (PNET) occurring as a second primary malignancy in childhood is exceedingly rare. We present a 7-year-old boy who developed a proven supratentorial PNET five years after enucleation and radio-/chemotherapy for a sporadic, unilateral retinoblastoma with optic nerve invasion. The association with this malignant eye disease as well as the effect of irradiation and multi-agent chemotherapy on second tumour induction are evaluated.

Medical subject headings