Isolated sacral agenesis in a fetus monosomic for 7q36.1-->qter.

Savage, N M; Maclachlan, N A; Joyce, C A; Moore, I E; Crolla, J A · J Med Genet · 1997

case_report · Level V

Where this comes from

Abstract

A fetus with severe sacral agenesis and intrauterine growth retardation, ascertained at prenatal diagnosis, was found to be carrying an unbalanced form of a paternal balanced reciprocal translocation (7;19)(q36.1;q13.43), resulting in functional monosomy for 7q36.1-->qter. Necropsy confirmed that the fetus had isolated sacral agenesis type II. A critical region for autosomal dominant sacral agenesis has recently been mapped to the 7q36 region. This case provides further evidence for a sacral agenesis locus in this region and may help to refine the critical region further.

Medical subject headings