Idiopathic torsion dystonia linked to chromosome 8 in two Mennonite families.

Almasy, L; Bressman, S B; Raymond, D; Kramer, P L; Greene, P E; Heiman, G A; Ford, B; Yount, J et al. · Ann Neurol · 1997

other · Level V

Where this comes from

Abstract

The DYT1 locus on chromosome 9q34 is responsible for most childhood limb-onset idiopathic torsion dystonia (ITD). Linkage to DYT1 has been excluded in families with adult-onset, and predominantly cranial-cervical, ITD. We mapped a locus (DYT6) associated with prominent cranial-cervical ITD in two large Mennonite families to chromosome 8. An identical haplotype spanning 40-cM segregates with ITD in these families, suggesting a shared mutation from the recent past.

Medical subject headings