Esophageal variceal bleeding caused by hypoplasia of the portal vein in a patient with the Klippel-Trenaunay syndrome.

Bataller, R; Sans, M; Escorsell, A; Elizalde, J I; Bosch, J; Rodés, J · Am J Gastroenterol · 1998

case_report · Level V

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Abstract

The case of a patient affected by Klippel-Trenaunay syndrome presenting with esophageal variceal bleeding caused by hypoplasia of the vena porta is reported. Hemostasis was achieved by performing a proximal spleno-renal shunt. We discuss the likely association of this mesodermal development abnormality and vascular disorders of the portal vein.

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