Nevoid basal cell carcinoma syndrome in a black child.

Hall, J; Johnston, K A; McPhillips, J P; Barnes, S D; Elston, D M · J Am Acad Dermatol · 1998

case_report · Level V

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Abstract

Nevoid basal cell carcinoma syndrome (NBCCS) is rare in black persons. We describe an 11-year-old black boy with NBCCS who presented with exotropia and a painful, expanding, cystic mass in the left posterior alveolar ridge. Further examination revealed odontogenic keratocysts with palmar and plantar pitting. Less than 5% of reported patients with NBCCS are black. To our knowledge, this is the first report of a black patient with NBCCS presenting with exotropia and an impacted molar displaced into the orbit by an odontogenic keratocyst.

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