Heritable connective tissue disorders in cervical artery dissections: a prospective study.
prospective_cohort · Level II
Where this comes from
- Record sourced from PubMed, PMID 9566419.
- No licence information is recorded for this record.
- Because redistribution is not established, this page shows the abstract only. Follow the links below for the full text.
Abstract
We prospectively evaluated 15 consecutive patients with spontaneous cervical artery dissections. Three patients (20%) had a heritable connective tissue disorder, each with a unique phenotype. None of these patients met the criteria of any of the named syndromes, and collagen and fibrillin analyses were normal. Heritable connective tissue disorders are common among patients with spontaneous cervical artery dissections, but, despite intensive investigations, the type of disorder usually cannot be identified. The underlying arteriopathy in cervical artery dissections is likely to be heterogeneous.
Medical subject headings
- Aortic Dissection
- Connective Tissue Diseases
- Intracranial Aneurysm